A case of Kawasaki disease initially diagnosed as septic shock
نویسندگان
چکیده
منابع مشابه
ZAP70 Related Severe Combined Immunodeficiency Initially Diagnosed as Incomplete (Atypical) Kawasaki Disease
ZAP70-related severe combined immunodeficiency (SCID) is a defect of the immune system characterized by absent or extremely low CD8+ T-cells and abnormal T-cell receptor signaling. This form of SCID is relatively rare with about 20 cases currently described in the literature and typically presents in infancy with recurrent opportunistic infections, failure to thrive, and gastrointestinal sympto...
متن کاملKawasaki Disease in Children: A Case Report.
SUMMARY: Kawasaki is an acute multisystemic disease affecting Predominantly. Children below 4 years of age. Having a Self- limited Course, it often Presents as Vasculitis. The Principal Complications are Stomatitis, conjunctivitis. Lymphadenopathy, Skin rashes as well as involvment of cardiovascular, alimentary and nervous system. In this article we report the First case of Kawasaki Disease ...
متن کاملKawasaki disease shock syndrome: a severe form of Kawasaki disease.
Kawasaki disease is a systemic vasculitis, primarily encountered in children. Its clinical presentation is well known, and coronary artery abnormalities are classical complications. Shock is not a common form of presentation of the disease. We report a case who presented with shock due to Kawasaki disease in accordance with the recently defined 'Kawasaki disease shock syndrome'. In pediatric in...
متن کاملPeriodic fever in MVK deficiency: a patient initially diagnosed with incomplete Kawasaki disease.
Mevalonate kinase deficiency (MKD) is a rare autosomal recessive disorder causing 1 of 2 phenotypes, hyperimmunoglobulin D syndrome and mevalonic aciduria, presenting with recurrent fever episodes, often starting in infancy, and sometimes evoked by stress or vaccinations. This autoinflammatory disease is caused by mutations encoding the mevalonate kinase (MVK) gene and is classified in the grou...
متن کاملPeriodic Fever in MVK Deficiency: A Patient Initially Diagnosed With Incomplete Kawasaki Disease abstract
Mevalonate kinase deficiency (MKD) is a rare autosomal recessive disorder causing 1 of 2 phenotypes, hyperimmunoglobulin D syndrome and mevalonic aciduria, presenting with recurrent fever episodes, often starting in infancy, and sometimes evoked by stress or vaccinations. This autoinflammatory disease is caused by mutations encoding the mevalonate kinase (MVK) gene and is classified in the grou...
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ژورنال
عنوان ژورنال: Journal of the Japanese Society of Intensive Care Medicine
سال: 2012
ISSN: 1340-7988,1882-966X
DOI: 10.3918/jsicm.19.405